摘要
IgG4相关硬化性胆管炎是IgG4相关疾病的胆道表现,被认为是自身免疫调节异常导致的纤维炎性过程,主要累及肝内和肝外大胆管。它被认为是一种良性疾病,通常对治疗反应良好,因此及早诊断并治疗是获得良好预后的根本。近年来该病发病率逐渐升高,然而目前对于该病的临床认识仍不普及,本文将对IgG4相关硬化性胆管炎的诊断标准、鉴别诊断以及目前的治疗作一综述。
IgG4-related sclerosing cholangitis is the biliary manifestation of IgG4-related disease.It is a fibroinflammatory process caused by abnormal autoimmune regulation,mainly involving intrahepatic and extrahepatic bile ducts.It is considered to be a benign disease and usually responds well to treatment.Therefore,early diagnosis and treatment are the basis for good recovery.In recent years,the prevalence of IgG4-related sclerosing cholangitis has gradually increased,but at present,the clinical understanding of the disease is still insufficient.This paper will review the diagnostic criteria,differential diagnosis and current treatment of IgG4-related sclerosing cholangitis.
作者
于佳丽
朱磊
YU Jiali;ZHU Lei(Department of Gastroenterology,the First Affiliated Hospital of Dalian Medical University,Dalian 116011,China)
出处
《大连医科大学学报》
CAS
2022年第5期456-459,465,共5页
Journal of Dalian Medical University
