期刊文献+

神经白塞氏病的早期诊断(附9例临床分析) 被引量:2

原文传递
导出
摘要 目的探讨神经白塞氏病的诊断和治疗特点,以期及早诊断和治疗,最大限度的降低病死率和致残率。方法对9例神经白塞氏病患者的临床资料进行回顾性分析。结果神经白塞病的发病率为7.6%,表现为视物模糊、复视3例,偏瘫3例,双下肢无力1例,失语、抽搐1例,意识障碍1例。病灶以脑干多见。结论神经白塞氏病的临床表现复杂而无特异性,诊断主要依赖于详细的病史询问,MRI和脑脊液检查有助于诊断和鉴别诊断。糖皮质激素和免疫抑制剂对神经白塞氏病有一定效果。早期诊断、规范治疗有利于降低病死率和致残率。
出处 《卒中与神经疾病》 2009年第6期363-365,共3页 Stroke and Nervous Diseases
  • 相关文献

参考文献7

  • 1International study group for Behcet's disease. Criteria for diagnosis of Behcet's disease. Laancet, 1990,335: 1078-10811.
  • 2Borhani Haghighi A, Pouimmand R, Nikseresht AR. Neuro-Behcet disease. A review. Neurologist, 2005,11 (2): 80-89.
  • 3Ho CL,Deruytter MJ. Manfestations of Neuro-Ne hect's disease. Report of two cases and review of the literature. Clin Neurol Neurosurg, 2005,107 (4) :310-314.
  • 4Benamour S, Naji T, Alaoui FZ, et al. Neurological involvement in Behcet's disease. 154 cases from a cohort of 925 patients and re view of the literature. Rev Neurol(Paris), 2006, 162 (11): 1{184- 1090.
  • 5Duvemoy HM, Human Brainstem Vessl, Berlin: Springer, 1978. 2-34.
  • 6白塞病诊治指南(草案)[J].中华风湿病学杂志,2003,7(12):762-764. 被引量:42
  • 7Kidd D, Steur A, Denman AM, et al. Neurological complications in Behcet's syndrome. Brain, 1999,122 (Pt 11 ): 2183-2194.

共引文献41

同被引文献17

  • 1武力勇,魏镜,李舜伟,陈琳,马中宏,郝红琳.神经白塞病28例临床特征分析[J].中华医学杂志,2006,86(11):779-781. 被引量:4
  • 2杨雪,贺茂林,刘利新,吴逊.急性脑血管病中的同侧舞蹈症和舞动症[J].中华神经科杂志,1996,29(4):222-224. 被引量:24
  • 3林仕芳,陈滢,林海谅,林艾羽,林弘.神经白塞病误诊2例报告并文献复习[J].中国误诊学杂志,2006,6(14):2673-2675. 被引量:1
  • 4赵贺玲,吕伟,郭洪伟,王晓玲,王树才,苏净,曹霞,曹秉振.神经白塞病三例临床病理分析[J].中华神经科杂志,2006,39(12):866-867. 被引量:3
  • 5江锋,杨岫岩,梁柳琴.白塞病并发血管性偏侧舞蹈症一例.中华风湿病学杂志,2001,5( 1): 34.
  • 6Gardner RC, Schmahmann JD. Ataxia and cerebellar atrophy-anovel manifestation of neuro-Behcet disease? Mov Disord, 2008,23(2):307-308.
  • 7Guak TH,Kim YI, Park SM, et al Paroxysmal focal dystonia inneuro-Behcet by a small ipsilateral thalamic lesion. Eur Neurol,2002,47(3):183-184.
  • 8Akman-Demir G,Serdaroglu P,Tasci B. Clinical patterns ofneurological involvement in Behcet's disease: evaluation of 200patients. The Neuro-Behcet Study Group. Brain,1999,122 Pt 11 :2171-2182.
  • 9Ohnishi J. Somatotropic lower monoballism following hemorrhage inthe subthalamic nucleus. Acta Neurol Scand, 1993,88( 1) :75-77.
  • 10ai-Araji A, Kidd DP. Neuro-Behcet's disease: epidemiology,clinical characteristics,and management. Lancet Neurol,2009,8(2):192-204.

引证文献2

二级引证文献1

相关作者

内容加载中请稍等...

相关机构

内容加载中请稍等...

相关主题

内容加载中请稍等...

浏览历史

内容加载中请稍等...
;
使用帮助 返回顶部